ICD-0-3 Entities

cases from the literature were (re-)classified according to ICD-O-3, as seemed appropriate according to the available information.

 ICD-O code or rangeCode translationCases
0000/0not classified in ICD-O 3 [e.g. non-neoplastic or benign]305
8000/3Neoplasm, malignant3
8010/2Carcinoma in situ, NOS10
8010/3Carcinoma, NOS85
8012/3Large cell carcinoma, NOS21
8013/3Large cell neuroendocrine carcinoma20
8020/3Carcinoma, undifferentiated type, NOS3
8021/3Carcinoma, anaplastic type, NOS39
8022/3Pleomorphic carcinoma1
8032/3Spindle cell carcinoma1
8033/3Sarcomatoid carcinoma4
8041/3Small cell carcinoma, NOS70
8046/3Non-small cell carcinoma6
8050/3Papillary carcinoma, NOS2
8052/0Squamous cell papilloma132
8070/1Premalignant squamous epithelium, NOS162
8070/2Squamous cell carcinoma in situ, NOS16
8070/3Squamous cell carcinoma, NOS1506
8071/0Squamous cell keratosis, NOS12
8075/3Squamous cell carcinoma, acantholytic2
8077/2Squamous intraepithelial neoplasia, grade III22
8090/3Basal cell carcinoma, NOS15
8120/2Transitional cell carcinoma in situ10
8120/3Transitional cell carcinoma, NOS251
8130/1Urothelial papilloma, NOS1
8130/2Papillary transitional cell carcinoma, non-invasive56
8130/3Papillary transitional cell carcinoma7
8140/0Adenoma, NOS319
8140/1atypical adenoma10
8140/2Adenocarcinoma in situ11
8140/3Adenocarcinoma, NOS2169
8144/3Adenocarcinoma, intestinal type197
8145/3Carcinoma, diffuse type8
8148/2Glandular intraepithelial neoplasia, grade III15
8150/1Islet cell adenoma8
8150/3Islet cell carcinoma18
8151/1Insulinoma, NOS28
8151/3Insulinoma, malignant7
8152/1Glucagonoma, NOS5
8152/3Glucagonoma, malignant8
8153/1Gastrinoma, NOS3
8153/3Gastrinoma, malignant5
8155/3Vipoma8
8156/1Somatostatinoma, NOS11
8160/3Cholangiocarcinoma78
8170/0Hepatocellular adenoma, NOS29
8170/3Hepatocellular carcinoma, NOS559
8171/3Hepatocellular carcinoma, fibrolamellar10
8200/3Adenoid cystic carcinoma55
8201/3Ductal carcinoma, cribriform type [C50._]2
8211/3Tubular adenocarcinoma5
8240/3Carcinoid tumor, NOS41
8246/3Neuroendocrine carcinoma71
8247/3Merkel cell carcinoma71
8249/3Atypical carcinoid tumor6
8250/3Bronchiolo-alveolar adenocarcinoma2
8260/3Papillary adenocarcinoma, NOS199
8271/0Prolactinoma13
8272/0Pituitary adenoma, typical47
8272/3Pituitary carcinoma, NOS4
8290/0Oncocytoma76
8290/3Follicular carcinoma, oxyphilic cell19
8310/3Clear cell renal cell carcinoma59
8312/3Renal cell carcinoma309
8317/3Renal cell carcinoma, chromophobe21
8319/3Renal medullary carcinoma9
8330/0Follicular adenoma, NOS16
8330/3Follicular adenocarcinoma, NOS27
8333/0Fetal adenoma10
8335/3Follicular carcinoma20
8337/3Insular carcinoma1
8340/3Papillary carcinoma, follicular variant8
8342/3Papillary carcinoma, oxyphilic cell1
8361/0Juxtaglomerular tumor [C64.9]2
8370/3Adrenal cortical carcinoma50
8380/1Endometrioid dysplasia37
8380/3Endometrioid carcinoma, NOS63
8384/3Adenocarcinoma, endocervical type14
8401/2Apocrine DCIS10
8401/3Apocrine adenocarcinoma4
8430/3Mucoepidermoid Carcinoma2
8441/3Serous carcinoma, NOS111
8442/1Serous cystadenoma, borderline malignancy21
8450/3Papillary cystadenocarcinoma, NOS2
8460/3Papillary serous cystadenocarcinoma123
8461/3Serous surface papillary carcinoma11
8470/3Mucinous cystadenocarcinoma, NOS19
8472/1Mucinous cystic tumor of borderline malignancy13
8480/3Mucinous adenocarcinoma52
8481/3Mucin-producing adenocarcinoma9
8490/3Signet ring cell carcinoma30
8500/2Ductal carcinoma in situ, NOS41
8500/3Infiltrating duct carcinoma, NOS916
8501/3Comedocarcinoma, NOS11
8503/2Noninfiltrating intraductal papillary adenocarcinoma1
8503/3Intraductal papillary adenocarcinoma with invasion2
8507/2Intraductal micropapillary carcinoma16
8510/3Medullary carcinoma, NOS90
8520/3Invasive lobular carcinoma64
8522/3Infiltrating duct and lobular carcinoma1
8523/3Infiltrating duct mixed with other types of carcinoma [C50._]4
8550/3Acinar cell carcinoma6
8560/3Adenosquamous carcinoma4
8562/3Myoepithelial carcinoma10
8576/3Hepatoid adenocarcinoma3
8581/3Thymoma, medullary [WHO A], malignant12
8585/3Thymoma, atypical [WHO B3], malignant17
8586/3Thymoma, type C [C37.9]10
8620/3Granulosa cell tumor, malignant56
8640/3Sertoli cell carcinoma1
8680/1Paraganglioma, NOS3
8682/1Parasympathetic paraganglioma16
8693/3Extra-adrenal paraganglioma, malignant8
8700/0Pheochromocytoma, NOS79
8700/3Pheochromocytoma, malignant14
8720/0Pigmented nevus, NOS76
8720/3Malignant melanoma, NOS178
8721/3Nodular melanoma9
8727/0Dysplastic nevus1
8742/3Lentigo maligna melanoma21
8744/3Acral lentiginous melanoma, malignant23
8761/3Malignant melanoma in congenital melanocytic nevus7
8770/0Epithelioid and spindle cell nevus29
8770/3Mixed epithelial and spindle cell melanoma2
8780/3Blue nevus, malignant5
8800/3Sarcoma, NOS25
8804/3Epithelioid sarcoma2
8805/3Undifferentiated sarcoma1
8810/0Fibroma, NOS3
8810/3Fibrosarcoma, NOS59
8811/0Fibromyxoid tumor, NOS1
8811/3Myxoinflammatory fibroblastic sarcoma6
8815/0Solitary fibrous tumor13
8815/3Solitary fibrous tumor, malignant4
8820/0Elastofibroma27
8821/1Desmoid-type fibromatosis30
8823/0Desmoplastic fibroma12
8825/0Myofibroblastic tumor, NOS1
8830/3Fibrous histiocytoma, malignant188
8850/0Lipoma, NOS27
8850/3Liposarcoma, NOS24
8851/3Liposarcoma, well differentiated55
8852/3Liposarcoma, myxoid13
8854/3Liposarcoma, pleomorphic18
8855/3Mixed type liposarcoma13
8858/3Liposarcoma, dedifferentiated13
8890/0Leiomyoma, NOS28
8890/3Leiomyosarcoma, NOS195
8891/3Epithelioid leiomyosarcoma1
8894/0Angioleiomyoma2
8895/3Myosarcoma2
8900/3Rhabdomyosarcoma, NOS17
8901/3Rhabdomyosarcoma, pleomorphic7
8920/3Alveolar rhabdomyosarcoma1
8930/3Endometrial stromal sarcoma3
8931/3Endometrial stromal sarcoma, low grade9
8936/0Gastrointestinal stromal tumor, benign102
8936/1Gastrointestinal stromal tumor, uncertain malignant potential112
8936/3Gastrointestinal stromal tumor, malignant260
8950/3Mullerian mixed tumor1
8951/3Mesodermal mixed tumor1
8960/3Nephroblastoma, NOS217
8964/3Clear cell sarcoma of kidney31
8970/3Hepatoblastoma127
8971/3Pancreatoblastoma1
8973/3Pleuropulmonary blastoma5
8980/3Carcinosarcoma, NOS23
8982/0Myoepithelioma13
8982/3Malignant myoepithelioma19
8990/3Mesenchymoma, malignant1
8991/3Embryonal sarcoma8
9010/0Fibroadenoma, NOS28
9020/0Phyllodes tumor, benign37
9020/1Phyllodes tumor, borderline17
9020/3Phyllodes tumor, malignant22
9040/3Synovial sarcoma, NOS42
9041/3Synovial sarcoma, monophasic75
9043/3Synovial sarcoma, biphasic29
9050/3Mesothelioma, NOS82
9051/3Desmoplastic mesothelioma59
9052/3Epithelioid mesothelioma, malignant64
9053/3Mesothelioma, biphasic, malignant27
9060/3Dysgerminoma17
9061/3Seminoma, NOS29
9063/3Spermatocytic seminoma12
9064/3Germinoma7
9070/3Embryonal carcinoma, NOS8
9071/3Yolk sac tumor21
9080/0Teratoma, benign22
9080/3Teratoma, malignant, NOS41
9081/3Teratocarcinoma2
9085/3Mixed germ cell tumor19
9100/0Hydatidiform mole7
9100/3Choriocarcinoma17
9101/3Choriocarcinoma combined w/ other germ cell elements2
9104/3Malignant placental site trophoblastic tumor2
9120/0Hemangioma, NOS10
9120/3Angiosarcoma10
9133/3Epithelioid hemangioendothelioma, malignant1
9140/3Kaposi sarcoma1
9150/1Hemangiopericytoma, NOS12
9160/0Angiofibroma, NOS54
9161/1Hemangioblastoma45
9180/3Osteosarcoma, NOS133
9182/3Fibroblastic osteosarcoma3
9183/3Osteosarcoma, telangiectatic1
9186/3Central osteosarcoma10
9220/3Chondrosarcoma, NOS79
9260/3Ewing sarcoma97
9270/3Odontogenic tumor, malignant2
9310/3Ameloblastoma, malignant29
9361/1Pineocytoma3
9362/3Pineal parenchymal tumor of intermediate differentiation6
9370/3Chordoma, NOS22
9380/3Glioma, NOS8
9381/3Gliomatosis cerebri22
9382/3Anaplastic oligoastrocytoma77
9390/1Choroid plexus papilloma, NOS41
9390/3Choroid plexus papilloma, malignant15
9391/3Ependymoma, NOS209
9392/3Ependymoma, anaplastic53
9394/1Myxopapillary ependymoma22
9400/3Astrocytoma, NOS84
9401/3Astrocytoma, anaplastic55
9412/1Desmoplastic infantile astrocytoma-ganglioglioma3
9421/1Astrocytoma, juvenile11
9424/3Pleomorphic xanthoastrocytoma50
9430/3Astroblastoma7
9440/3Glioblastoma, NOS420
9442/3Gliosarcoma23
9450/3Oligodendroglioma, NOS53
9451/3Oligodendroglioma, anaplastic42
9470/3Medulloblastoma, NOS208
9471/3Desmoplastic medulloblastoma46
9472/3Medullomyoblastoma1
9473/3Primitive neuroectodermal tumor, NOS45
9474/3Large cell medulloblastoma21
9490/0Ganglioneuroma1
9490/3Ganglioneuroblastoma8
9500/3Neuroblastoma, NOS507
9503/3Neuroepithelioma, NOS1
9505/1Ganglioglioma62
9506/1Neurocytoma10
9510/3Retinoblastoma, NOS135
9522/3Olfactory neuroblastoma17
9530/0Meningioma, NOS92
9530/3Meningioma, malignant60
9532/3Fibrous meningioma, malignant2
9535/3Hemangioblastic meningioma, malignant10
9540/0Neurofibroma, NOS64
9540/3Malignant peripheral nerve sheath tumor70
9560/0Schwannoma, NOS61
9581/3Alveolar soft part sarcoma14
9582/0Granular cell tumor7
9590/3Malignant lymphoma, NOS32
9591/3Malignant lymphoma, B-cell NOS5
9650/3Hodgkin lymphoma, NOS27
9651/3Classical Hodgkin lymphoma, lymphocyte-rich8
9652/3Classical Hodgkin lymphoma, mixed cellularity, NOS21
9653/3Classical Hodgkin lymphoma, lymphocyte depletion, NOS2
9659/3Hodgkin lymphoma, nodular lymphocyte predominance19
9663/3Classical Hodgkin lymphoma, nodular sclerosis, NOS19
9673/3Mantle cell lymphoma338
9678/3Primary effusion lymphoma11
9679/3Mediastinal large B-cell lymphoma89
9680/3Diffuse large B-cell lymphoma, NOS740
9684/3ML, large B-cell, diffuse, immunoblastic, NOS16
9687/3Burkitt lymphoma, NOS83
9689/3Splenic marginal zone lymphoma, NOS65
9690/3Follicular lymphoma, NOS270
9691/3Follicular lymphoma, grade 263
9695/3Follicular lymphoma, grade 147
9698/3Follicular lymphoma, grade 314
9699/3Marginal zone lymphoma, NOS116
9700/3Mycosis fungoides152
9701/3Sezary syndrome255
9702/3Malignant lymphoma, T-cell NOS46
9705/3Peripheral T-cell lymphoma, NOS62
9709/3Malignant lymphoma, T-cell NOS, cutaneous9
9714/3Anaplastic large cell lymphoma, NOS105
9716/3Hepatosplenic gamma/delta T-cell lymphoma2
9717/3Enteropathy type T-cell lymphoma71
9718/3Anaplastic large cell lymphoma, cutaneous type59
9719/3NK/T-cell lymphoma24
9727/3Precursor cell lymphoblastic lymphoma, NOS1
9728/3Precursor B-cell lymphoblastic lymphoma2
9729/3Precursor T-cell lymphoblastic lymphoma1
9731/3Plasmacytoma, NOS54
9732/3Plasma cell myeloma253
9733/3Plasma cell leukemia15
9734/3Plasmacytoma, extramedullary21
9742/3Mast cell leukemia1
9750/3Malignant histiocytosis1
9751/1Langerhans cell histiocytosis, NOS7
9761/3Waldenstrom macroglobulinemia1
9765/1Monoclonal gammopathy7
9823/3B-cell chronic lymphocytic leukemia/small lymphocytic lymphoma646
9826/3Acute lymphoblastic leukemia, mature B-cell type31
9827/3Adult T-cell leukemia/lymphoma [HTLV-1 pos.]82
9833/3Prolymphocytic leukemia, B-cell type6
9834/3Prolymphocytic leukemia, T-cell type42
9835/3Acute lymphoblastic leukemia, NOS272
9836/3Precursor B-cell lymphoblastic leukemia280
9837/3Precursor T-cell lymphoblastic leukemia108
9840/3Acute erythroid leukemia [FAB M6]7
9860/3Myeloid leukemia, NOS1
9861/3Acute myeloid leukemia, NOS247
9866/3Acute promyelocytic leukemia [FAB type M3]6
9867/3Acute myelomonocytic leukemia [FAB type M4]31
9871/3Acute myelomonocytic leukemia with abnormal marrow eosinophils [FAB M4Eo]3
9872/3Acute myeloblastic leukemia with minimal differentiation [FAB type M0]3
9873/3Acute myeloblastic leukemia without maturation [FAB type M1]18
9874/3Acute myeloblastic leukemia with maturation [FAB M2]27
9875/3Chronic myelogenous leukemia20
9891/3Acute monoblastic leukemia without differentiation [FAB M5a]20
9895/3Acute myeloid leukemia with prior myelodysplastic syndrome6
9910/3Acute megakaryoblastic leukemia [FAB M7]13
9920/3Therapy-related acute myeloid leukemia, NOS1
9940/3Hairy cell leukemia36
9945/3Chronic myelomonocytic leukemia, NOS3
9948/3Aggressive NK-cell leukemia6
9950/3Polycythemia vera29
9961/3Chronic idiopathic myelofibrosis26
9962/3Essential thrombocythemia8
9963/3Chronic neutrophilic leukemia1
9980/3Refractory anemia, NOS26
9982/3Refractory anemia with ringed sideroblasts [RARS]12
9983/3Refractory anemia with excess blasts [RAEB]21
9984/3Refractory anemia with excess blasts in transformation [RAEBT]26
9985/3Refractory cytopenia with multilineage dysplasia2
9986/3Myelodysplastic syndrome with 5q- syndrome3
9989/3Myelodysplastic syndrome, NOS3
Progenetix collects information about the genomic copy number profiles of individual cancer and leukemia cases. It consists mainly of a compilation of published data from chromosomal and array/matrix Comparative Genomic Hybridization (CGH) experiments. Progenetix is with 17255 CGH and 2443 array CGH experiments the largest public CGH database. The software and database content are maintained by Michael Baudis.